Gorlin syndrome — multiple odontogenic keratocysts in the mandible.

Nevoid basal cell carcinoma syndrome (Gorlin syndrome) is autosomal dominant, caused by PTCH1 mutations, and presents with multiple OKCs, multiple BCCs at a young age, palmar/plantar pits, calcification of the falx cerebri, and skeletal anomalies (bifid ribs, kyphoscoliosis). Multiple jaw radiolucencies with scalloped borders are the hallmark.